Fundamentals:
- Defidiency in liver isozyme of Glycogen Phosphorylase
- Accumulation of Glycogen
- Improves with age
Causes:
Genetic:
- Hereditary
Route Of Transmission ROT:
LOC:
Pathogenesis:
Symptoms:
- Hepatomegally
- Hypoglycemia
- Variable
- Asymptomatic
- Liver damage
- Stunted growth